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Table 1 Reported cases of hepatic PEComa. Review of the literature [34,35,36,37,38,39,40,41,42,43,44,45,46,47,48,49]

From: Unresectable hepatic PEComa: a rare malignancy treated with stereotactic body radiation therapy (SBRT) followed by complete resection

No

Author

Age/sex

Tx

Follow-up [months]

Outcome

Imaging of primary tumor

Imaging for follow-up

1

Sheng et al.

55/M

OP

12

NED

MRI

MRI

2

Paiva et al.

51/F

OP

25

NED

CT

n/a

3

Sanchez-Perez et al.

32/F

OP

n/a

n/a

CT/MRI

n/a

4

Cheung et al.

53/F

OP

12

NR

CT

CT

5

Zhao et al.

58/M

OP

9

NR

US, CT

n/a

6

Patra et al.

50/F

OP

24

NED

CT

n/a

7

Fang et al.

56/F

OP

24

NED

CT

n/a

8

Ameurtesse et al.

63/F

OP (not R0)

9

NED

US, CT, MRI

n/a

9

Khaja et al.

51/F

n/a

n/a

n/a

US, FDG-PET/CT, MRI

n/a

10

Jafari et al.

53/F

OP

14

NED

CT, MRI

CT, MRI

11

Zhang et al.

63/F

OP

8

NED

CT

n/a

12

Zimmermann et al.

53/M

OP

17

NED

US, FDG-PET/CT, MRI

n/a

13

Panahova et al.

38/M

OP

6

NR

US, CT, MRI

 

14

Ahn et al.

36/F

OP

3

NED

CT

n/a

15

Della Vigna et al.

46/F

OP

n/a

n/a

US, MRI

n/a

16

Maebayashi et al.

58/M

OP

60

NED

CT, MRI

n/a

17

Liu et al.

25/F

OP

12

NR

US, CT, MRI

n/a

18

Yu et al.

41/F

OP

9

NED

US, CT

n/a

19

Jurado et al.

45/F

OP

n/a

n/a

CT

n/a

20

Selvaggi et al.

42/M

OP

< 1

fatal

CT

n/a

21

Akitake et al.

36/F

OP

18

NED

US, CT, MRI

n/a

  1. Tx therapy, NED no evidence of disease, US ultrasound